///2017 Abstract Details
2017 Abstract Details2019-08-02T15:54:53-06:00

The anesthetic management of an urgent cesarean section in a patient with Goldenhar syndrome: a case report

Abstract Number: T-71
Abstract Type: Case Report/Case Series

Dina Aboutouk BSc. MD. FRCPC1 ; Leo Jeyaraj MD, FRCA2; Jennifer Racine BSc, MD, FRCPC3; George Dumitrascu BSc, MD, ABAD4; Joseph Desreux BSc, MD5; Xiao Xu Chen BSc, MD6


Goldenhar Syndrome (GS), also called oculoauriculovertebral spectrum or syndrome, is a relatively rare congenital condition (1). Exact etiology is not known but believed to be due to abnormal embryonic vascular supply to the first and second arch (2). Common characteristics include hemifacial microsomia, facial hypoplasia, lateral facial cleft, dental abnormalities, microtia, anotia and an unusually small mouth (3,4,5). Systemic manifestations may include heart, kidney, lung and spinal abnormalities (6,7). Fertility and longevity are not directly affected (8). Despite this, there are only two reported cases outlining the anesthetic management of pregnant patients with GS in the literature (9,10). We present a case outlining the anesthetic management of a 21-year-old pregnant women with GS presenting for an urgent cesarean section complicated by an intra-operative failed airway and a severe adverse reaction while managing postpartum hemorrhage. This case will not only add to the reported cases in the literature but will also outline the necessary steps required to safely manage patients with such a congenital disease. This is a unique patient population that should be managed at a tertiary care centre with high volume of high risk obstetrical patients with a standardized approach that include pre-operative multi-disciplinary planning and the involvement of multiple health care workers to ensure patient safety.


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9)Hezelgrave NL, Srinivas K, Ahmad I, Mascarenhas L. Use of awake oral fibreoptic intubation (AFOI) for caesarian section in a woman with Goldenhar Syndrome: a case report. Eur J Obstet Gynecol Reprod Biol. 2011 Dec;159(2):479-80.

10)Lokhande C, Riad I, Tetzlaff J, Ayad S. The peri-operative management of a cesarean section in a patient with Goldenhar syndrome (GS): A case report. J Clin Anesth. 2016 Nov;34:448-51.

SOAP 2017